Q ) Most common indication for Pediatric liver transplant (DNB SS)
A. Biliary atresia
B. Metabolic diseases
C. Alagille syndrome
MOst common cause or liver transplant in children. Presents as persistent jaundice after birth. Etiology is not clear
Findings include absent extrahepatic ducts and gallbladder. Biopsy is diagnostic
Q) Not true about recurrent pyogenic cholangitis :
a) Mostly there are intrahepatic strictures with involvement of the left side duct
b) It can present as choledochoduodenal fistula
c) In it there is complete biliary obstruction which leads to marked jaundice and pruritis
d) MRCP and other other cholangiography can be diagnostic
In recurrent pyogenic cholangitis (RPC) complete obstruction does not occur and jaundice and pruritis is not marked. RPC is a disease commonly seen in young Asians (also known as oriental cholangiohepatitis) which leads to multiple strictures in extra or intrahepatic ducts.
Association with Ascaris lumbricoides and Clonorchis sinensis has been noted.
It can present as choledocholithiasis with stricture, choledochoduodenal fistula, acute pancreatitis, secondary biliary cirrhosis and can lead to cholangiocarcinoma.
MRCP can be diagnostic and is preferred because of its non invasive nature.
Q) False about choledochal cyst is
a) Type IV is also known as Caroli's disease
b) Type I choledochal cyst is the most common type
c) Type III is also called as choledochocele
d) Type II choledochal cyst is diverticular disease
Answer is for premium members
This question was asked in NEET this year and a similar question on choledochal cyst is already on the website for some time.