Q) An young male with cholangitis, EHPVO + Portal Biliopathy was drained with a plastic biliary stent next step?

a) Repeat biliary Stenting every 3 months then followed up

b) Replace plastic to bare metal stent

c) Prepare for Lineorenal shunt surgery

d) Do MRCP and proceed accordingly

Points  about Portal Biliopathy

Portal biliopathy (PB) is a clinical condition defined as the presence of abnormalities in the biliary tree (including biliary tree and gallbladder) in patients with non-cirrhotic/non-neoplastic extrahepatic portal vein obstruction (EHPVO) and portal cavernoma.

The spectrum of biliary abnormalities include both  intra- and extra-hepatic biliary stenosis (single or multiple)

With or without consensual above dilation

Bile duct wall irregularity or thickening

Bile duct angulation

Varicose veins located at the ductular walls and gallbladder

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