Management of various Hereditary Syndromes

Q) Total Proctocolectomy is required for which of the following ? ( MCH GI Surgery Question- Click here for all) 

a) Cowden

b) HNPCC

c) Gardner

d) PJS  

Snippet -- HNPCC- Lynch syndrome patients develop colorectal and extracolonic cancers at a young age. It accounts for approximately 3% of all CRCs, and 10% to 19% of CRCs diagnosed before age 50. Read on..........

Cowden

Q) Not seen in cowden syndrome
A. NET
B. Hamartoma
C. CA breast
D. Bowel malignancy

Malignancy risk in CS is significant outside the GI tract. Women have a 50% lifetime risk of developing breast cancer ...............

Read on ..............